Work

Moyamoya syndrome in sickle cell anaemia: a cause of recurrent stroke

Year: 2014

Type: article

Abstract: Summary We report a case with interesting imaging findings as well as an unfortunate but not unexpected clinical outcome. Our patient, an 8-year-old Jamaican boy of Afro-Caribbean descent with homozygous sickle cell disease, presented with left-sided upper limb weakness. He had a history of recurrent cerebrovascular accidents and transient ischaemic attacks beginning at 4 years of age. MRI revealed old bilateral infarctions and the ivy sign on fluid-attenuated inversion recovery sequences. MR angiography demonstrated numerous collaterals, most apparently arising from the left internal carotid, consistent with moyamoya syndrome. The patient had a full recovery and remained well for almost 2 years when he suffered another stroke.

Source: BMJ Case Reports

DOI: 10.1136/bcr-2014-203727

Authors: Deanne Soares, Richard Bullock, Susanna Ali

Institutions: University of the West Indies System, University of the West Indies

Language: English

Topic: Moyamoya disease diagnosis and treatment

Subfield: Clinical Neurology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: bronze

OpenAlex ID: W2000947108