Work

Hypothermic cardiopulmonary bypass in paramyotonia congenita: a case report.

Year: 1983

Type: article

Abstract: Paramyotonia congenita is a non-progressive disease characterised by myotonia (failure of muscle relaxation) induced by the exposure of the affected muscles to cold.Episodes of flaccid paralysis occur and may be related to hyperkalaemic periodic paralysis.Proximal myopathy or muscular hypertrophy may occur.The condition is inher- ited as an autosomal dominant.'Severe paralysis may occur with comparatively slight increases in plasma potas- sium concentration.During an attack of paralysis there is loss of potassium from muscle cells, which become depolarised.

Source: Thorax

DOI: 10.1136/thx.38.6.476

Authors: I J Reece, J A Kennedy, J A Simpson, K M Taylor

Institutions: Glasgow Royal Infirmary, University of Glasgow

Language: English

Topic: Cardiac and Coronary Surgery Techniques

Subfield: Surgery

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: bronze

OpenAlex ID: W2005123204