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Hyperhemolysis in a patient with β-thalassemia major

Year: 2009

Type: article

Abstract: A case of hyperhemolysis in a 2-year-old boy with beta thalassemia major was noted. After several transfusions, he developed hyperhemolysis with a positive (C3d only) direct antiglobulin test (DAT) and no clinically significant RBC allo- or auto-antibodies. (There was a weak cold antibody, showing a narrow thermal range). Because there was no significant improvement with steroid and immunoglobulin infusions, cyclophosphamide therapy was tried with notable success.

Source: Asian Journal of Transfusion Science

DOI: 10.4103/0973-6247.45259

Authors: RLakmali Morawakage, B.J.C Perera, P.D.N Dias, SK Wijewardana

Institutions: National Blood Transfusion Service, Lady Ridgeway Hospital for Children

Language: English

Topic: Hemoglobinopathies and Related Disorders

Subfield: Genetics (clinical)

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W2018560040

FWCI:

Cites: 14

Cited by: 12

Related to: 10