Work

Successful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion

Year: 2016

Type: article

Abstract: Fat embolism syndrome (FES) is a rare complication of sickle-cell disease (SCD) associated with extremely high mortality rates. It affects predominantly non-SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life-saving.

Source: Clinical Case Reports

DOI: 10.1002/ccr3.727

Authors: Paul Greaves, Vivek Mathew, Catherine Peters, Susan Rowe, Roger J. Amos, Dimitris A. Tsitsikas

Institutions: National Health Service, Homerton University Hospital, Homerton University Hospital NHS Foundation Trust

Language: English

Topic: Hemoglobinopathies and Related Disorders

Subfield: Genetics (clinical)

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $1,820