Work

Anaesthesia and orphan disease: airway and anaesthetic management in Huntington’s disease

Year: 2017
Type: article
Study design: Case Report
Abstract: We present a case that highlights the issues surrounding the delivery of a safe general anaesthetic to a patient with Huntington's disease (HD) and bulbar dysfunction. In the case of a 46-year-old patient undergoing laparoscopic percutaneous endoscopic gastrostomy tube insertion, we discuss the rationale behind our chosen method and anaesthetic agents as well as airway issues specific to HD. In a patient whose condition would not allow for an awake fibreoptic intubation, we opted for a modified rapid sequence induction. Special considerations were made with regard to muscle relaxation given the complications associated with inadequate paralysis and reversal in patients with HD. The technique we describe may also apply to other patient categories, such as patients with movement disorders, bulbar dysfunction and dementia.
Authors: Phuong Thao Nguyen, Daveena Meeks, Despoina Liotiri
Language: English
Field: Medicine
Open Access status: bronze
OpenAlex ID: W2766338165
FWCI: 0.677
Cites: 14
Cited by: 6
Related to: 10