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Biphasic renal synovial sarcoma with extensive venous tumor thrombosis: A rare presentation

Year: 2018

Type: article

Abstract: Primary renal synovial sarcoma (SS) is a very rare soft-tissue tumor arising from the kidney. These tumors histologically closely resemble other sarcoma variants. Immunohistochemical and cytogenetic techniques remain the cornerstone in achieving the correct diagnosis. Radical surgical excision is the primary treatment for local tumor control and alleviation of symptoms. Adjuvant chemotherapy, at present, has only a limited role. We report a unique case of a 21-year-old young male with the diagnosis of a biphasic renal SS with extensive venous system thrombosis involving the inferior vena cava, bilateral iliac, and femoral vessels which was managed by radical nephrectomy and tumor thrombectomy followed by adjuvant chemotherapy.

Source: Urology Annals

DOI: 10.4103/ua.ua_9_18

Authors: Ramanathinam Manikandan, UmaKant Dutt, LalgudiNarayanan Dorairajan, BheemanathiHanuman Srinivas

Institution: Jawaharlal Institute of Post Graduate Medical Education and Research

Language: English

Topic: Sarcoma Diagnosis and Treatment

Subfield: Oncology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $100