Work

Complete heart block in a young adult with non-isolated congenitally corrected transposition of the great arteries: Case report

Year: 2022

Type: article

Abstract: Introduction and importance: Congenitally corrected transposition of the great arteries (ccTGA) or L-looped transposition of the great arteries (L-TGA) is a very rare and complex form of congenital heart disease. The majority of patients with ccTGA have at least one or more associated congenital heart disorders, essentially ventricular septal defects. Patients with ccTGA can remain asymptomatic for a long time and the diagnosis can sometimes be made late in life at the stage of complications. Case presentation: Here, we report a rare case of a 19-year-old patient, with no medical or surgical history, presenting a complete heart block as initial presentation of a ‘’non-isolated” ccTGA. The diagnosis is made essentially by echocardiography. This case aims to show diagnostic difficulties of this rare congenital heart disease and be aware of the risk of its relative complications. HIGHLIGHTS Congenitally corrected transposition of the great arteries (ccTGA) is a very rare and complex form of congenital heart disease. Cardiac conduction disorders are well-established complications of ccTGA. The presence or absence of associated cardiac disorders is an important parameter to determinate the risk of chronic heart failure.

Source: Annals of Medicine and Surgery

DOI: 10.1016/j.amsu.2022.103500