Acute interstitial pneumonia due to amyopathic dermatomyositis
Year: 2022
Type: article
Study design: Case Report
Abstract: Clinically amyopathic dermatomyositis usually presents with severe skin rashes but no muscle involvement and is associated with the highly lethal form of rapidly progressive interstitial lung disease. Diagnosis of myositis-related acute interstitial pneumonia can be particularly challenging, as the clinical presentation of hypoxia and respiratory failure has a broad differential diagnosis. This is especially true when the characteristic skin or muscle finding are absent and the patient has no history of idiopathic inflammatory myopathies. We present a rare case of a patient who presented with rapidly worsening acute respiratory failure from acute interstitial pneumonia due to an undiagnosed amyopathic dermatomyositis with positive anti-MDA5 autoantibody without any of the typical myositis symptoms or physical exam findings.
Authors: Simón Esteva, Erin Tuttle, He Huang, Nishith Mewada
Institution: Baylor University Medical Center
Language: English
Subfield: Rheumatology
Field: Medicine
Domain: Health Sciences
Open Access status: green
OpenAlex ID: W4293399708